Browsing Tıp Fakültesi by Subject "Familial hemophagocytic lymphohistiocytosis"
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Hacettepe Üniversitesi Tıp Fakültesi Çocuk Hematoloji Ünitesi'nde İzlenen Familyal Hemofagositik Lenfohistiyositoz Hastalarının Değerlendirilmesi
(Tıp Fakültesi, 2013)Familial hemophagocytic lymphohistiocytosis (FHL) is an autosomal recessive, life-threatening condition characterized by deficient immune response. The major underlying defect in FHL is impaired Natural Killer (NK) cell ...