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dc.contributor.authorBeder, Sumru
dc.contributor.authorErsoy, Zinet Gui
dc.contributor.authorGullu, Emine
dc.contributor.authorUtine, G. Eda
dc.contributor.authorKayacan, Oya
dc.contributor.authorKarnak, Demet
dc.date.accessioned2019-12-10T11:33:09Z
dc.date.available2019-12-10T11:33:09Z
dc.date.issued2010
dc.identifier.issn1300-0292
dc.identifier.urihttps://doi.org/10.5336/medsci.2008-8689
dc.identifier.urihttp://hdl.handle.net/11655/16089
dc.description.abstractNoonan syndrome (NS), is an autosomal dominant disorder commonly seen in childhood and is characterized by short stature, congenital heart defects and facial abnormalities (especially in adults) along with thoracic deformity. Lymphatic dysplasia can be seen with this syndrome causing chylothorax by development of fistulas between thoracic duct and pleural space or it can directly occur by malformation of thoracic lymphatic vessels. Hence, chylothorax can also be seen. Herein, we present a case with this syndrome and chylothorax secondary to possible lymphatic dysplasia. We achieved a great success with ocreotide and medium chain trigliserides in the management of chylothorax and hence suggest this therapy to other clinicians.
dc.language.isoen
dc.publisherOrtadogu Ad Pres & Publ Co
dc.relation.isversionof10.5336/medsci.2008-8689
dc.rightsinfo:eu-repo/semantics/openAccess
dc.subjectGeneral & Internal Medicine
dc.titleSuccessful Ocreotide and Medium-Chain Triglyceride Therapy for Cylothorax in a Patient with Noonan Syndrome: Case Report
dc.title.alternativeNoonan Sendromlu Bir Olguda Oktreotid ve Orta Zincirli Yağ Asitleri Kullanılarak Şilotoraksın Başarılı Tedavisi
dc.typeinfo:eu-repo/semantics/article
dc.typeinfo:eu-repo/semantics/publishedVersion
dc.relation.journalTurkiye Klinikleri Tip Bilimleri Dergisi
dc.contributor.departmentTıbbi Genetik
dc.identifier.volume30
dc.identifier.issue4
dc.identifier.startpage1402
dc.identifier.endpage1405
dc.description.indexWoS
dc.description.indexScopus


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