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IL1RN Variation Influences Both Disease Susceptibility and Response to Recombinant Human Interleukin-1 Receptor Antagonist Therapy in Systemic Juvenile Idiopathic Arthritis
(Wiley, 2018)
Objective. To determine whether systemic juvenile idiopathic arthritis (JIA) susceptibility loci that were identified by candidate gene studies demonstrate association with systemic JIA in the largest study population ...
2012 Revised International Chapel Hill Consensus Conference Nomenclature Of Vasculitides
(Wiley-Blackwell, 2013)
Consensus Treatment Plans For Chronic Nonbacterial Osteomyelitis Refractory To Nonsteroidal Antiinflammatory Drugs And/Or With Active Spinal Lesions
(Wiley, 2018)
Objective. To develop standardized treatment regimens for chronic nonbacterial osteomyelitis (CNO), also known as chronic recurrent multifocal osteomyelitis (CRMO), to enable comparative effectiveness treatment studies. ...
International Retrospective Chart Review of Treatment Patterns in Severe Familial Mediterranean Fever, Tumor Necrosis Factor Receptor-Associated Periodic Syndrome, and Mevalonate Kinase Deficiency/Hyperimmunoglobulinemia D Syndrome
(Wiley, 2017)
Objective. Periodic fever syndrome (PFS) conditions are characterized by recurrent attacks of fever and localized inflammation. This study examined the diagnostic pathway and treatments at tertiary centers for familial ...
Colchicine Resistance And Intolerance In Familial Mediterranean Fever: Definition, Causes, And Alternative Treatments
(W B Saunders Co-Elsevier Inc, 2017)
Background: Familial Mediterranean Fever (FMF) is a hereditary autoinflammatory syndrome characterized by recurrent serositis or arthritis attacks and, in some patients, chronic subclinical inflammation that predisposes ...
Registries in Rheumatological and Musculoskeletal Conditions. Paediatric Behcet'S Disease: An International Cohort Study of 110 Patients. One-Year Follow-Up Data
(Oxford Univ Press, 2011)
Methods. International experts have defined the inclusion criteria as follows: recurrent oral aphthosis (ROA) plus one of following-genital ulceration, erythema nodosum, folliculitis, pustulous/acneiform lesions, positive ...
Endothelial Function In Patients With Familial Mediterranean Fever-Related Amyloidosis And Association With Cardiovascular Events
(Oxford Univ Press, 2014)
Objectives. Secondary amyloidosis is the most important complication of FMF and endothelial function is more severely impaired. Elevated asymmetric dimethyl arginine (ADMA) may mediate the excess cardiovascular disease ...
Development Of The Autoinflammatory Disease Damage Index (Addi)
(BMJ, 2017)
Objectives Autoinflammatory diseases cause systemic inflammation that can result in damage to multiple organs. A validated instrument is essential to quantify damage in individual patients and to compare disease outcomes ...
A Preliminary Score for The Assessment of Disease Activity in Hereditary Recurrent Fevers: Results From The Aidai (Auto-Inflammatory Diseases Activity Index) Consensus Conference
(BMJ, 2011)
Background The systemic autoinflammatory disorders (SAID) share many clinical manifestations, albeit with variable patterns, intensity and frequency. A common definition of disease activity would be rational and useful in ...
Consensus Classification Criteria For Paediatric Behcet'S Disease From A Prospective Observational Cohort: Pedbd
(BMJ, 2016)
Background We aimed to describe the main features of Behcet's disease (BD) in children in the largest prospective cohort to date and to propose a classification. Methods An international expert consensus group was formed ...