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Molecular Diagnosis Of Shwachman-Diamond Syndrome Presenting With Pancytopenia At An Early Age: The First Report From Turkey
(Springer India, 2013)
A three-month-old boy presented with growth failure, skeletal abnormalities, otitis media and pancytopenia. Exocrine pancreatic insufficiency was confirmed by low levels of fecal elastase. He was diagnosed as Shwachman-Diamond ...
The Glycocalyx and Trauma: A Review
(Lippincott Williams & Wilkins, 2016)
In the United States trauma is the leading cause of mortality among those under the age of 45, claiming approximately 192,000 lives each year. Significant personal disability, lost productivity, and long-term healthcare ...
Hematologically Important Mutations: Leukocyte Adhesion Deficiency (First Update)
(Academic Press Inc Elsevier Science, 2012)
Leukocyte adhesion deficiency (LAD) is an immunodeficiency caused by defects in the adhesion of leukocytes (especially neutrophils) to the blood vessel wall. As a result, patients with LAD suffer from severe bacterial ...
Update On The Safety And Efficacy Of Retroviral Gene Therapy For Immunodeficiency Due To Adenosine Deaminase Deficiency
(Amer Soc Hematology, 2016)
Adenosine deaminase (ADA) deficiency is a rare, autosomal-recessive systemic metabolic disease characterized by severe combined immunodeficiency (SCID). The treatment of choice for ADA-deficient SCID (ADA-SCID) is hematopoietic ...
Splenic Artery Embolization: An Alternative Approach In A Critically Ill Patient With Autoimmune Hemolytic Anemia
(Aves Yayincilik, 2011)
Assessment of general health status and hematological parameters usually precedes the use of invasive diagnostic and therapeutic procedures in critically ill patients. Angiography can be effective and safe as a substitute ...
Atraumatic Osteonecrosis After Estrogen Replacement Therapy Associated with Low Protein S Level in a Patient with Turner Syndrome
(Sage Publications Inc, 2010)
Atraumatic osteonecrosis has been associated with a variety of clinical conditions including corticosteroid usage, alcoholism, infections, hyperbaric events, storage disorders, marrow-infiltrating diseases, coagulation ...
Clinical Investigation Of Oral Findings In Inherited Disorders Of Platelet Function
(Aves Yayincilik, 2011)
Objective: Bleeding disorders are a very important health problem due to the associated high risk of hemorrhage during dental procedures. The present study aimed to investigate oral manifestations of inherited disorders ...
European Guidelines For Empirical Antibacterial Therapy For Febrile Neutropenic Patients In The Era Of Growing Resistance: Summary Of The 2011 4Th European Conference On Infections In Leukemia
(Ferrata Storti Foundation, 2013)
Owing to increasing resistance and the limited arsenal of new antibiotics, especially against Gram-negative pathogens, carefully designed antibiotic regimens are obligatory for febrile neutropenic patients, along with ...
Prohemostatic and Antithrombin Activities of Ankaferd Hemostat are Linked To Fibrinogen Gamma Chain and Prothrombin by Functional Proteomic Analyses
(Sage Publications Inc, 2012)
Ankaferd blood stopper (ABS) is a novel topical hemostatic agent of plant origin registered for the management of external hemorrhages, in Turkey. The ABS-induced formation of the protein network with vital erythroid ...
Rebound Thrombocytosis Following Induction Chemotherapy Is An Independent Predictor of A Good Prognosis in Acute Myeloid Leukemia Patients Attaining First Complete Remission
(Karger, 2015)
There are very few data about the relationship between acute myeloid leukemia (AML) prognosis and bone marrow recovery kinetics following chemotherapy. In this study, we aimed to assess the prognostic importance and clinical ...